ACHONDROPLASIA

ENDOCRINOLOGY DIVISION DEPARTMENT OF CHILD HEALTH MEDICAL SCHOOL, UNIVERSITY OF SUMATERA UTARA

An 11-year old Saudi girl

The Saudi Dental Journal (2010) 22, 1959

Intraoral views showing dental caries, anterior open bite, anterior reversed jet, posterior cross bite and class III dental malocclusion.

Lateral skull radiograph revealed retrognathic maxilla, with normal position of the mandible, and skeletal class III jaw relation.

Medical Care
Closely monitor growth : Weight, height, and

occipitofrontal circumference (OFC) monthly for the first year of life. Measure the upper-to-lower segment ratio. Monitor developmental milestones in gross and fine motor, language and social/adaptive. Perform careful neurologic examinations. Manage frequent middle ear infections and address any concern for hearing loss. Orthodontic evaluation for dental malocclusion and crowding. Control weight to prevent obesity and associated

Surgical Care
Leg-lengthening procedures using distraction

osteogenesis. In children with signs of craniomedullary compression, surgical treatment to release the compression can improve neurologic, cognitive, and respiratory functions. Lumbar laminectomy can be performed for spinal stenosis, Spinal fusion for persistent kyphosis Dentists treating these children should be able to recognize these features and its